A rare case of VACTERL association with a genito-urinary anomaly

نویسندگان

چکیده

VACTERL association is a cipher used to describe cluster of conditions wherein there seemingly unexplainable non-random specific birth defects multiple organ systems. It includes vertebral anomalies (V), anal (A), cardiac (C), tracheoesophageal fistula (TEF), renal (R) or radial bone (R), and limb (L). At least three these seven malformations need be present constitute the association. Other congenital different systems may additionally with this but are classified separately rarity occurrence greater than even We report neonate abnormalities system atrial septal defect ventricular defect, H type, multicystic dysplastic kidney. Additionally, baby was also found have micropenis, genito-urinary anomaly. With optimal surgical correction in post-natal period vigilant periodic follow-up, prognosis relatively positive. Medical management can as therapy for treating long-term sequelae if any. Therefore, morbidity mortality prevented great extent early diagnosis immediate intervention.

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Case Report: VACTERL association

VACTERL association is a useful acronym for a condition characterised by the sporadic, non-random association of specific birth defects of multiple organ systems.We present one such case which had congenital abnormalities of renal,skeletal and cardiac system.

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A Rare Case of Pulmonary Artery Sling with the VACTERL Association in a 20-Month-Old Infant

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ژورنال

عنوان ژورنال: International Journal of Contemporary Pediatrics

سال: 2022

ISSN: ['2349-3283', '2349-3291']

DOI: https://doi.org/10.18203/2349-3291.ijcp20223429